Protein : PCK2

Name PCK2
Description phosphoenolpyruvate carboxykinase 2 (mitochondrial)
Owner Public
URN urn:agi-llid:5106
Connectivity 41
Notes This gene encodes a member of the phosphoenolpyruvate carboxykinase (GTP) family. The protein is a mitochondrial enzyme that catalyzes the conversion of oxaloacetate to phosphoenolpyruvate in the presence of GTP. A cytosolic form encoded by a different gene has also been characterized and is the key enzyme of gluconeogenesis in the liver. The encoded protein may serve a similar function, although it is constitutively expressed and not modulated by hormones such as glucagon and insulin that regulate the cytosolic form. Alternatively spliced transcript variants have been described. Results suggest that pepck2 gene expression is regulated by its 5' flanking region up to 822 bp, and 317 bp upstream of transcriptional start point.
Hugo ID 8725

Microarray ID 128860_at
1425615_a_at
1452620_at
97398_at
aa044561_s_at
msa.15442.0_s_at
msa.27764.0_s_at
msa.31074.0_s_at
A_51_P110888
37188_at
86118_at
202847_at
X92720_at
73397_at
A_23_P140207
A_14_P115524
A_23_P128817
OH2666
ST053

GenBank ID CR608041
CR609997
CR611857
CR613166
CR616177
CR618266
NC_000014
NM_001018073
NM_004563
NP_001018083
NP_004554
NT_026437
NT_086806
Q16822
X92720
Y11484
AAH10318
AAH23437
AK007429
51493278
4758885
4758886
51472041
2661751
2661752
34526637
34783904
12655193
48145942
48145943
1403049
1403050
3287892
51768594
28077028
28077029
12840975
26326494
26326495
26327466
26327467
26330305
26330306
16307538
16307539
19484089
19484090
52783203
AK030501
AK031612
BC010318
BC023437
BC028326
NC_000080
NM_028994
NP_083270
NT_039606
Q8BH04
AK034927
AK142561
AK147972
AK161944
AK165094
AK170242
AK189946
AK210790
AK214165
AK218043
AK218547
AK219654
BAC26991
BAC27477
BAC28883
BAE25104
BAE28259
BAE41656
AAH01454
AK129934
BC001454
BX248272
CAA63380
CAA72272
CAD62600
CAG33194
CR456913
CR602594

Chromosome position 14q11.2
14 21.0 cM

GO ID 0000166
0004613
0005525
0005739
0006094
0016829
0030145
0004611
0016831

Alias 9130022B02Rik
mitochondrial phosphoenolpyruvate carboxykinase 2
mitochondrial Phosphoenolpyruvate carboxykinase precursor (GTP)
PCK2
PEPCK
PEPCK2
PEPCK-M
Phosphoenolpyruvate carboxykinase, mitochondrial precursor (GTP)
Phosphoenolpyruvate carboxylase 2
RIKEN cDNA 9130022B02 gene
Phosphoenolpyruvate carboxylase II
phosphoenolpyruvate carboxykinase 2 (mitochondrial)
PEPCK-Ms
PEPCK2s
gAF1/PCK2
1810010O14Rik
RIKEN cDNA 1810010O14 gene
mitochondrial phosphoenolpyruvate carboxykinase II

Organism Mus musculus
Homo sapiens

MedLine Reference 14651853
8645161

LocusLink ID 69057
110830
5106
74551
56186

FunctionalClass GTP binding
lyase
manganese ion binding
nucleotide binding
phosphoenolpyruvate carboxykinase (GTP)
carboxy-lyase
phosphoenolpyruvate carboxykinase

Hugo Symbol PCK2

Unigene ID Hs.75812
Mm.29856

KEGG pathway Citrate cycle (TCA cycle)
Pyruvate metabolism

GO Cellular Component mitochondrion

Cell Localization Mitochondria

Pathway EGF-ERBB3
EGF-ERBB4
EGF-LRP8
EGF-NGFR
INS-HLA-DRB1
INS-TFRC
LEP-LRP2
TGFB1-ACVR1B
TGFB1-ACVR2
TGFB1-ACVR2B
TGFB1-ACVRL1
TGFB1-BMPR1B
TGFB1-IGF2R
TGFB1-SELE
TGFB1-TGFBR1
TGFB1-TGFBR2
TGFB1-TGFBR3
Full DuPont
DuPont 2
DuPont 4
PPAR all
PPARgamma
PGC1alpha
RXR
GR
COUP-TF
HNF4a
NR common targets

GO Biological Process gluconeogenesis

Group Gtp binding proteins
Full DuPont

EC Number 4.1.1.32

MGI ID 1860456

Swiss-Prot Accession Q16822

OMIM ID 261650

Source Curated